Fetal Center


Inherited Arrhythmias: Long QT Syndrome

The Challenge
Long QT syndrome (LQTS) is a disorder of cardiac repolarization. It is characterized by a prolongation of the QT interval, and a predisposition to ventricular tachyarrhythmias, which are associated with syncope, arrhythmic events, and sudden cardiac death (SCD). In recent years, there have been significant advances in understanding the genetic basis of the syndrome. Newer genetic forms of LQTS have been identified, too, plus a laboratory test has become available to help in the diagnosis of the syndrome. As knowledge of LQTS continues to expand, clinical applications of this growing body of information need further study


Fetal coronary fistula

Prenatal diagnosis and perinatal management of left coronary
artery to right atrium fistula

G. MIELKE*, L. SIEVERDING†, T. BORTH-BRUNS†, K. EICHHORN‡, D. WALLWIENER* and
U. GEMBRUCH§

Departments of *Obstetrics and Gynecology and †Pediatric Cardiology, University of Tuebingen, ‡Medical Practice, Weimar and §Department of
Obstetrics and Gynecology, University of Luebeck, Germany

KEYWORDS: Coil embolization, Coronary artery fistula, Echocardiography, Fetal circulation, Fetal heart, Prenatal diagnosis
Ultrasound Obstet Gynecol 2002; 19: 612–615


CONGENITAL CORONARY ARTERY FISTULAS

CONGENITAL CORONARY ARTERY FISTULAS: CLINICAL
CONSIDERATIONS AND SURGICAL TREATMENT
GOU-JIENGHONG,* CHIH-YUANLIN,* CHUNG-YILEE,* SHIN-HURNLOH,† HOU-SHENGYANG,*KUANG-YILIU,* YI-TINGTSAI*AND CHIEN-SUNGTSAI*
*Division of Cardiovascular Surgery, Department of Surgery, and † Department of Pharmacology, Tri-Service General Hospital, National Defense Medical Center, Taipei, Taiwan, China

ANZ J. Surg. 2004; 74: 350–355

Background:
Coronary artery fistulas are uncommon abnormalities that can cause significant cardiac morbidity. Indications for operation vary, particularly, for asymptomatic patients. Early surgical correction is indicated because of the high incidence of late symptoms and complications.


Twin-twin transfusion syndrome

Obstetrics and Gynecology

Prenatal cardiovascular manifestations in the twin-to-twin transfusion syndrome recipients and the impact of therapeutic amnioreduction

Catherine Barrea, MD – a-, Fawaz Alkazaleh, MD -b-, Greg Ryan, MB -b-, Brian W. McCrindle, MD -a-, Anita Roberts, BSc -a-, Jean-Luc Bigras, MD -a-, Jon Barrett, MD -c-, Gareth P. Seaward, MB -b- , Jeffrey F. Smallhorn, MB, BS -a-, Lisa K. Hornberger, MD -a*.

Evaluated the cardiovascular pathologic condition in the recipient twin in twin-to-twin transfusion syndrome and the influence of amnioreduction.


Prenatal diagnosis of congenital heart disease

Prenatal diagnosis of congenital heart disease using four-dimensional spatio-temporal image correlation (STIC) telemedicine via an Internet link: a pilot study
F. Viñals 1 *, L. Mandujano 2, G. Vargas 3, A. Giuliano 1

1Centro AGB Ultrasonografía, Clinica Sanatorio Alemán, Concepción, Chile, 2Centro Medico El Bosque, Punta Arenas, Chile
3Hospital La Serena, La Serena, Chile

email: F. Viñals (fvinals55@hotmail.com)

*Correspondence to F. Viñals, Avda Sanhueza 55. 403 A, Concepción, Chile

Keywords
4D • congenital heart disease • prenatal diagnosis • spatio-temporal image correlation • STIC • telemedicine
t


Double-Orifice Mitral Valve

Double-Orifice Mitral Valve with Intact Atrioventricular Septum: An
Echocardiographic Study With Anatomic and Functional Considerations
Bibhuti B. Das, MD, Linda B. Pauliks, MD, Ole A. Knudson, Jr, RDCS, Scott Kirby, RDCS,
Kak-Chen Chan, MD, Lilliam Valdes-Cruz, MD, and Raul O. Cayre, MD,

Denver, Colorado;
Boston, Massachusetts; and Corrientes, Argentina